呼吸 Kartagener syndrome 支扩、副鼻窦炎、右位心三联征

卡塔格内综合征(Kartagener syndrome,KS)又称家族性支气管扩张症, 又称支气管扩张-副鼻窦炎-内脏转位综合征，是原发纤毛运动障碍综合征的一种, 是一种少见的先天遗传性疾病。Kartagener综合征(Kartagener's syndrome,KS) 临床上主要表现为以反复呼吸道化脓性感染、咯血为特征的支气管扩张症状及副鼻窦炎和右位心.三联征。该症特征性的CT表现为:内脏转位、支气管扩张及副鼻窦炎. Kartagener综合征,属于罕见疾病，其临床发病率为1/4万～1/ 5万.

Recurrent respiratory tract infections secondary to abnormal respiratory mucociliary function because of a generalized deficiency of dynein arms of cilia. Will also affect auditory epithelium and sperm tails. Diagnosed by triad of Situs inversus (including dextrocardia), sinusitis, and bronchiectasis(1.)

Kartagener's syndromeAlso known as:Afzelius’ syndrome，Kartagener’s triad，Zivert's syndrome，Zivert-Kartagener triad

Synonyms:Immotile cilia syndrome, ciliary dyskinesia, bronchiectasis-dextrocardia-sinusitis, sinusitis-bronchiectasis-situs inversus syndrome, situs inversus-sinusitis-bronchiectasis, dextrocardia-bronchiectasis-sinusitis immotile cilia, dextrokardia-bronchiektasis-sinusitis-syndrom (German).