呼吸 Congenital Lobar Emphysema

Marked hyperexpansion of left upper lobe with collapse of left lower lobe and mediastinal shift.

General

Progressive overdistension of lobe at birth
Male predominance 3:1
Associated with CHD in 15% (PDA,VSD)
Symptoms: respiratory distress (90%) and cyanosis <>

Mortality: 10%

Treatment: surgical resection

Etiology

Immaturity of bronchial cartilage

Endobronchial obstruction (fold, web, mucus)

Bronchial compression from vascular structure e.g. PDA, aberrant left pulmonary artery

Location
LUL 43%，RML 35%，RUL 20%，Two lobes involved 5%

X-ray Appearance

Mass-like opacity following birth

Lucency develops over next two weeks

Air-trapping occurs in affected lobe

Compression atelectasis of adjacent lobes

Shift of mediastinum away from lesion

http://www.learningradiology.com/lectures/chestlectures/conglobaremphysemappt_files/frame.htm