Except for its unilateral localization, the gross and histological findings of URCD 单侧多囊肾病 are indistinguishable from those of autosomal dominant polycystic kidney disease 常染色体显性多囊肾病 (ADPKD)However, unlike ADPKD, URCD patients show neither a genetic background nor progressive deterioration in renal function.
Besides ADPKD, multilocular cystic renal neoplasms, cystic dysplasia and multiple simple cysts are other categories of cystic diseases.
Multilocular cystic renal neoplasms 多房囊性肾瘤 usually form discrete, encapsulated masses that are well demarcated from the adjacent renal parenchyma. Also, a cystic neoplasm grows slowly and expands to displace normal renal parenchyma and does not contain the islands of enhancing parenchyma on CT, which are found in URCD.
A multicystic dysplastic kidney 多囊性肾发育不良 is usually diffusely cystic, severely dysplastic and non-functioning due to ureteropelvic occlusion. It is usually easily distinguished from URCD with sonography, CT and radionuclide studies. The collecting system draining the dysplastic segment is atretic or obstructed and, therefore, is not usually opacified on contrast-enhanced CT, whereas the collecting system in URCD shows only the displacement.
Multiple simple cysts may be difficult to distinguish from URCD when confined to one kidney. However, they are not as numerous as in URCD.
http://ndt.oxfordjournals.org/cgi/content/full/14/8/1999
Besides ADPKD, multilocular cystic renal neoplasms, cystic dysplasia and multiple simple cysts are other categories of cystic diseases.
Multilocular cystic renal neoplasms 多房囊性肾瘤 usually form discrete, encapsulated masses that are well demarcated from the adjacent renal parenchyma. Also, a cystic neoplasm grows slowly and expands to displace normal renal parenchyma and does not contain the islands of enhancing parenchyma on CT, which are found in URCD.
A multicystic dysplastic kidney 多囊性肾发育不良 is usually diffusely cystic, severely dysplastic and non-functioning due to ureteropelvic occlusion. It is usually easily distinguished from URCD with sonography, CT and radionuclide studies. The collecting system draining the dysplastic segment is atretic or obstructed and, therefore, is not usually opacified on contrast-enhanced CT, whereas the collecting system in URCD shows only the displacement.
Multiple simple cysts may be difficult to distinguish from URCD when confined to one kidney. However, they are not as numerous as in URCD.
http://ndt.oxfordjournals.org/cgi/content/full/14/8/1999
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